Cystic Fibrosis Level 3

CysticFibrosis (CF)
What is it?
*Cystic Fibrosis- Heredity Disease that causes glands to produce
Fluids that affect the Digestive Tract and the Lungs
*Most Common- Inherited Disease leading to Death in the U.S.
among white people
Signs and Symptoms:
*High levels of- Sodium/Na and Chloride/Cl in tears, saliva, sweat
*Thick secretions- in pancreas, bile ducts, small intestine, bronchi
Who does is affect?
*1 in 2,000- live births, 80-90% have pancreatic insufficiency,
85% growth retardation
-Average Life Span- 24 years (improving up to 30-40 now)
-Death often from- Malnutrition, Lungs Collapse, Cor Pulmonale,
Bronchopneumonia, Lung Transplantation with some good results
What can I do?
*See your Physician
*Visit Your Local Health Department
*See FFF Registered Dietitian- on line for help
-Fats- may not be well tolerated, Lactose intolerance is common,
use Soft Foods if chewing causes fatigue
-Encourage fish- for the fatty acids
*Healthy Weight- avoid anorexia due to respiratory distress
*Protein- for growth, resistance to infection, development
*Replace- electrolytes as loss in vomiting